Evolution and survival time from diagnosis differ depending on ILD type. In addition, within a particular disease group, such as the IIPs, the prognosis may be very different depending on subclassification: although the 5-year survival rate is only about 20% in IPF, it is about 60% in lymphoid interstitial pneumonia, 80% in cellular nonspecific interstitial pneumonia and close to 100% in cryptogenic organising pneumonia. In a UK study, 5-year survival with EAA was 82% in the period 1993–2004. In sarcoidosis, 5-year survival is estimated to be well above 90%.

See the entire Interstitial lung diseases Chapter